successful treatment of unilateral klippel-trenaunay syndrome with pulsed-dye laser in a 2-week old infant
نویسندگان
چکیده
introduction: klippel–trenaunay syndrome (kts) is a rare congenital mesodermal abnormality characterized by varicose veins, cutaneous capillary malformation, as well as bone and soft tissue hypertrophy. case report: a 2-week-old female infant presented to our clinic because of vascular nevus and progressive enlargement of her right extremities and trunk since birth. the patient was treated with 595-nm pulsed-dye laser (pdl). her port-wine stain (pws) disappeared completely after third pdl session and the soft tissue hypertrophy stopped. the patient experienced neither recurrence nor any change in size after 7 years of follow up. conclusion: pdl can treat kts completely with no reccurence if it is used in “early stage” of disease.
منابع مشابه
Successful pulmonary thromboendarterectomy in a patient with Klippel-Trenaunay syndrome.
Klippel-Trenaunay syndrome (KTS) is a congenital disorder characterized by a triad of cutaneous vascular nevi, soft tissue or bony hypertrophy, and varicose veins or venous malformations involving one or more extremities. An incidence of venous thromboembolism of up to 22% has been reported in this disorder. Also reported is the development of chronic thromboembolic pulmonary hypertension (CTEP...
متن کاملKlippel-Trenaunay Syndrome
Figure 1. Asymmetric hypertrophy of the left arm and in particular the left first and second digit macrodactyly.
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The Klippel-Trenaunay Syndrome is a triad of congenital anomalies characterized by a vascular naevus, varicose veins and hypertrophy of soft tissue and bone. A number of patients affected with this rare syndrome need amputation. In this paper the systemic problems, stump complications and prosthetic difficulties of four amputees with Klippel-Trenaunay syndrome are outlined. The period of follow...
متن کاملKlippel-Trenaunay Syndrome
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متن کاملCME Klippel-Trenaunay Syndrome
Learning Objectives: After studying this article, the participant should be able to: 1. Define the triad of signs and symptoms that describe Klippel-Trenaunay syndrome. 2. Speculate on the various theories regarding its pathogenesis. 3. Discuss the necessary radiologic workup required to pursue appropriate management. 4. Restate the most common reasons for surgically treating this syndrome. 5. ...
متن کاملKlippel-Trenaunay syndrome: diagnosis in a neonate.
Pereira C, et al. BMJ Case Rep 2017. doi:10.1136/bcr-2017-221011 Description A male newborn was evaluated due to a port-wine stain. Mother, 40 years old, father and brother were healthy. Gestation was uneventful. Amniocentesis revealed a normal male karyotype. A caesarean delivery was performed at 38 weeks. First physical examination showed a port-wine stain affecting the abdomen, back and left...
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عنوان ژورنال:
journal of lasers in medical sciencesجلد ۸، شماره ۲، صفحات ۹۸-۱۰۰
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